|
Frequency (%) |
Cholestatic liver disease |
63 |
Biliary atresia
Other: Progressive familial intrahepatic cholestasis, sclerosing cholangitis,
Alagille syndrome, TPN-induced cholestasis |
|
Fulminant hepatic failure |
11 |
Metabolic liver disease
Wilson disease, alpha-1-antitrypsin deficiency, tyrosinemia,
Urea cycle defects such as ornithine transcarbamylase deficiency,
glycogen storage disease |
13 |
Malignancies (hepatoblastoma, HCC) |
4 |
Other |
9 |
|