Table 4

Abnormality	Grading per abnormality		Anatomical regions scored
	Percentage disease extent	Score
Pure ground-glass opacity Fibrosis (including thickened reticular markings, bronchiectasis and bronchiolectasis) Honeycombing	0 1-25% 26-50% 51-75% >75%	0 1 2 3 4	Zone 1: Apex to aortic arch Zone 2: Aortic arch to inferior pulmonary veins Zone 3:Inferior pulmonary veins to diaphragms Right and left lung scored separately

Table 4: Semi-quantitative scoring; Scleroderma Lung Study [27].