Variable

Disease

Category

Estimate

Count

Proportion

lcSSc

Female:Male

18.0:1

18:1

dcSSc

Female:Male

1.2:1

6:5

Severity
Index

lcSSc

7.00 ± 0.78

18

dcSSc

7.18 ± 0.91

11

Modified Rodnan

lcSSc

9.05 ± 1.29

19

Skin Score

dcSSc

22.82 ± 2.82

11

Age

lcSSc

58.53 ± 2.50 yr

19

dcSSc

49.64 ± 3.17 yr

11

Duration

lcSSc

10.68 ± 2.68 yr

19

dcSSc

2.91 ± 0.48 yr

11

Lung

ILD

lcSSc

47.4 ± 11.5 %

19

dcSSc

63.6 ± 14.5 %

11

Putative
PAH

lcSSc

47.4 ± 11.5 %

19

dcSSc

36.4 ± 14.5 %

11

FVC
Predicted

lcSSc

86.6 ± 4.5 %

18

dcSSc

73.4 ± 6.5 %

11

DLCO

lcSSc

63.1 ± 4.9 %

19

Predicted

dcSSc

64.8 ± 8.3 %

10

Telangiectasia

lcSSc

17.6 ± 9.2 %

17

dcSSc

20.0 ± 12.6 %

10

Digits

Raynaud’s

lcSSc

100 %

18

dcSSc

100 %

11

Active digital ulcers

lcSSc

35.3 ± 11.6 %

17

dcSSc

30.0 ± 14.5 %

10

No. of digits with

lcSSc

0.71 ± 0.28

17

Active digital ulcers

dcSSc

0.88 ± 0.48

9

Contracture of

lcSSc

41.2 ± 11.9 %

17

phalanges

dcSSc

63.6 ± 14.5 %

11

Autoantibodies

ACA positive

lcSSc

15.8 ± 8.4%

19

dcSSc

0 %

11

ANA positive

lcSSc

84.2 ± 8.4%

19

dcSSc

90.1 ± 8.7%

11

Scl-70 positive

lcSSc

15.8 ± 8.4%

19

dcSSc

72.7 ± 13.4%

11

Treatment

Methotrexate

lcSSc

0 %

19

dcSSc

18.2 ± 11.6 %

11

Cyclophosphamide

lcSSc

0 %

19

dcSSc

45.5 ± 15.0 %

11

Except where indicated otherwise, values are the mean ± SE.

Table 1: Demographics.