| |
Classic |
Hypomyopathic |
Amyopathic |
Juvenile |
Patient |
| Mean age at diagnosis (years) |
51.9 |
65.9 |
48.5 |
6.8 |
59 |
| Hallmark skin lesions |
erythema of the knuckles with a raised violaceous scaly eruption, violaceous hue on the upper eyelids, a flat red rash on the face and upper trunk |
+ |
| Proximal muscle weakness |
+ |
- |
- |
+/- |
- |
| Total CK level |
Elevated |
Elevated |
Normal |
Normal or elevated |
Normal |
| Myopathy |
+ |
+/- |
- |
+/- |
- |
| Lung pathology |
Interstitial lung disease, respiratory muscle insufficiency, or aspiration pneumonia |
Interstitial lung disease |
|
