| |
Patients without MEFV mutations
n=96
n (%) |
Patients with MEFV mutations
n=6
n (%) |
| Mean age at diagnosis (years): |
7,1±3,9 |
5,8 ±2,6 |
| Gender, n (%) |
|
|
| Female |
51 (53) |
3 (50) |
| Male |
45 (47) |
3 (50) |
| Clinical features, n (%) |
|
|
| Palpable purpura |
96 (100) |
6 (100) |
| Arthritis or periatricular edema |
55 (57) |
3 (50) |
| Mild GIT involvement |
21 (22) |
1 (17) |
| Severe GIT involvement |
11 (12) |
0 |
| Renal involvement |
10 (10) |
1 (17) |
| Laboratory findings: |
|
|
| Leukocytes, n1=96, n2=6 |
9,7±3,9 |
9,1±2,9 |
| Elevated ESR, n1= 51, n2=4 |
26,0±19,3 |
26,8±21,1 |
| Elevated CRP, n1=27 n2=1 |
32,3±21,9 |
18* |
* CRP value was higher than 5mg/L in only one patient with MEFV mutation
n1- number of data available for patients without MEFV mutations
n2- number of data available for patients with MEFV mutations |
