Characteristic feature Total (n=31 pts)
Ocular symptoms  
Asymptomatic 10
Decreased vision 13
Floaters 11
Visual acuity  
Better than 20/40 26
20/50-20/200 18
Worse than 20/200 8
Fixes and follows 8
Enucleated at presentation 2
Intraocular pressure (mean, median; range) mm Hg 16.3, 16; 4-34
Fundus examination Eyes (n=62)
Vitreous abnormalities 60
Lattice degeneration 13
Giant retinal tear 2
Retina detachment 5
Treatment  
Laser 14
Cryotherapy 1
Combination therapy 6
Observation 40
Retina abnormalities in fellow eye  
Exensive lattice degeneration 5
Retina tears 16
Retina detachment 7
Duration to develop retina detachment in fellow eyes (mean, median; range), months 40.7, 22.5; 5-123
Treatment of fellow eyes  
Prophylactic scleral buckle in fellow eyes 5
Laser 15
Cryotherapy 1
Combination treatment (vitrectomy, laser, cryo,± scleral buckle) 7
Table 2: Ophthalmic features at initial presentation, (n=31 pts, 62 eyes).