Individual Age at the time of examination Arden ratio Visual Acuity Fundus examination II4 38 Y LE- 1.119; Time to peak- 15.0 min RE- 1.099; Time to peak- 14.8 min BE- 6/12 NIP Macula - Egg yolk like appearance of macula with pseudohypopyon stage III1 9 Y LE- 1.398; Time to peak- 1.0 min RE- 1.480; Time to peak- 2.2 min LE- 6/12 RE- 6/18 (Visual field- Vision with pin hole) LE- Macula- Normal RE- Macula- Oval lesions seen just infero nasal to macula III 2 7 Y (non-co-operative) BE- 6/6 BE- Macula - Normal

LE: Left Eye; RE: Right Eye; BE: Both Eyes; NIP: Not Improved with Pinhole

Table 1: Clinical documentation of the individuals with Best disease – SEB1 (at the time of recruitement-2009).