| Author |
Age/Gender |
Site |
Size (cm) |
Clinical status (UICC) |
Treatment |
Follow-Up |
| Kleinsasser et al. [1] |
57/M |
Hard palate |
“Hazelnut in size” |
NI |
Extirpation |
NI |
| Chen [10] |
60/F |
Tongue |
“Lump” |
NI |
Wide excision |
NED 5 years |
| Pesce et al. [11] |
62/F |
Oral vestibule |
1.5 |
NI |
Excision |
NI |
| Zohar et al. [12] |
47/M |
Upper lip |
1 |
NI |
Wide excision |
NED 2 years |
| Watatani et al. [13] |
60/F |
Tongue |
0.4 |
T1N0M0 |
Wide excision |
NED 4 years |
| Kumar et al. [14] |
NI (2 cases) |
Maxilla |
NI |
NI |
NI |
NI |
| Delgado et al. [15] |
42/M |
Hard palate |
3 |
T2N0M0 |
Maxillectomy |
DOD 5.2 years |
| Epivatianos et al. [16] |
80/M |
Upper vestibular sulcus |
2.5 |
T2N0M0 |
Maxillectomy |
NI |
| 74/M |
Lower vestibular sulcus |
4 |
T2N2cM0 |
Wide excision-ND |
DOD 2 years |
| 58/M |
Hard palate |
4 |
T2N2bM0 |
RT |
DOD 6 months |
| 60/M |
Buccal sulcus |
3 |
T2N0M0 |
Maxillectomy-ND-RT |
NED 4 years |
| Yoshimura et al. [5] |
62/M |
Buccal mucosa |
3.1 |
T2N2bM0 |
Radical surgery-RT |
Alive after 1.6 years with multiple metastases |
| Tatemoto et al. [6] |
58/F |
Hard palate |
1 |
T1N0M0 |
Local resection |
NED 2.5 years |
| Guzzo et al. [17] |
NI |
Cheek |
NI |
TxN0M0 |
Enucleated |
Alive with disease (54 months) |
| Suzuki & Hashimoto [18] |
56/M |
Mandible |
4 |
NI |
Excision |
NED 5 years |
| Lopes et al. [19] |
63/M |
Hard palate |
6 |
T4N2bM0 |
Hemimaxillectomy-ND-RT |
DOD 11 months |
| Huh et al. [20] |
61/M |
Hard palate |
5 |
T3N0M0 |
Hemimaxillectomy-ND-RT |
NED 9 months |
| 54/M |
Hard palate |
5 |
T3N0M0 |
Hemimaxillectomy |
NED 15 months |
| 23/F |
Hard Palate |
4 |
T4N0M1 |
Patient denied further treatment |
DOD 7 months |
| Van Heerden et al. [21] |
53/F |
Hard palate and right alveolar ridge |
14 |
T4N-M0 |
Patient refused treatment |
Lost to follow-up |
| 71/M |
Hard palate and buccal sulcus |
5 |
T4N-M0 |
Patient refused treatment |
Lost to follow-up |
| 57/M |
Hard palate |
6 |
T4N-M0 |
Patient refused |
Lost to follow-up |
| treatment |
| 63/F |
Hard palate |
7 |
T4N-M0 |
Hemimaxillectomy-ND-RT |
NED 10 Months |
| 47/M |
Hard palate |
5 |
T4N-M0 |
Patient still considering surgical treatment |
NI |
| Cheuk et al. [22] |
44/F |
Buccal mucosa |
1.2 |
T1N0M0 |
Local excision |
NED 4 years |
| Ide et al. [23] |
45/F |
Retromolar gingiva |
1.5 |
T1N0M0 |
Local excision |
NED 11 years |
| Jaehne et al. [24] |
NI (5 cases) |
NI |
NI |
stage II (n=1), stage IV(n=4) |
NI |
NED (20%), DOD (80%) |
| Ponniah et al. [25] |
26/M |
Hard palate |
3 |
T2N0M0 |
Local excision |
NED 4 years |
| Suzuki et al. [26] |
64/F |
Tongue |
1.5 |
T1N0M0 |
Partial glossectomy |
NED 2.5 years |
| KikuchiĀ et al. [27] |
62/M |
Mandible |
ND |
stage III |
Hemimandibulectomy-ND-RT-ChT |
NED 5 years |
| Dhanuthai et al. [28] |
NI |
AlveolarĀ mucosa |
NI |
NI |
NI |
NI |
| Thamilselvi et al. [29] |
35/F |
Soft palate |
5.5 |
T3N0M0 |
Local excision |
NI |
| Present cases |
80/M |
Buccal fornix |
1 |
T1N0M0 |
Hemimaxillectomy |
NED 6 years |
| 64/M |
Soft palate |
3 |
T2N2cM0 |
Radical tumor resection-ND |
DOD 1 month |
ChT, chemotherapy; DOD, died of disease; F, female; M, male; N/A, not available; ND, neck dissection; NED, no evidence of disease; RT, radiotherapy; NI, no
information. |