| Case (year) |
Sex |
Age at diagnosisof PBC (years) |
Age at diagnosis of ITP (years) |
PBC prior to ITP |
Scheuer’s classification |
Complications |
Remarks |
References |
| 1(1987) |
F |
60 |
60 |
Sim |
1? |
|
Familial PBC |
[22] |
| 2(1987) |
F |
43 |
43 |
Sim |
|
|
Insulin receptor autoantibodies(+) |
[23] |
| 3(1989) |
F |
59 |
59 |
Sim |
|
|
|
[24] |
| 4(1990) |
F |
63 |
67 |
+ |
|
|
|
[21] |
| 5(1996) |
M |
59 |
59 |
Sim |
2 |
|
|
[25] |
| 6(1997) |
F |
35 |
41 |
+ |
|
|
Liver transplantation |
[26] |
| 7(1998) |
F |
<60 |
62 |
+ |
|
|
Liver transplantation |
[27] |
| 8(2001) |
M |
37 |
37 |
Sim |
1? |
|
|
[28] |
| 9(2004) |
F |
64 |
34 |
- |
|
AIH, Hashimoto’s thyroiditis |
|
[29] |
| 10(2007) |
F |
81 |
81 |
Sim |
|
AIHA(Evans syndrome) |
|
[30] |
| 11(2007) |
M |
44 |
59 |
+ |
|
AIHA(Evans syndrome), Hypothyroidism |
Liver transplantation |
[31] |
| 12(2008) |
F |
67 |
74 |
+ |
3 |
|
Sepsis → death |
[19] |
| 13(2009) |
F |
58 |
58 |
Sim |
3? |
AIH, Scleroedema |
|
[32] |
| 14(2009) |
M |
55 |
55 |
Sim |
|
AIHA(Evans syndrome), Sjögren’s syndrome |
|
[33] |
| 15(2011) |
F |
40 |
40 |
Sim |
2? |
AIH, Polymyositis |
|
[34] |
| 16(2012) |
M |
45 |
42 |
|
2? |
IgG4-related cholangitis |
|
[35] |
| 17(2013) |
F |
53 |
53 |
Sim |
2? |
AIHA(Evans syndrome) |
|
[6] |
| PBC: primary biliary cirrhosis; ITP: immune thrombocytopenic purpura; F: female; M: male; Sim: simultaneous;AIH: autoimmune hepatitis; AIHA: autoimmune hemolytic anemia |