Progressive pt number Sex Age Nails % Area damaged mouth eyes Larynx Oesophagus Scarring of hands Skin cancer Chronic wound (>50%) Scarring alopecia Nutritional compromise Total
1 M 1 2 30 3 2 0 2 1 x x x 0 40
2 F 2 3 40 5 5 0 5 1 x x x 5 64
3 F 3 4 35 3 3 0 3 3 x x x 5 56
4 F 6 5 30 3 3 0 2 4 0 2 0 4 53
Table 1: EBDR score, according to BEBS score, for patients with age ranging from 0 to 6 years.