| oral ulceration |
1 point |
| genital ulceration |
2 points |
| Skin lesions (pseudofolliculitis, erythema nodosum) |
1 point |
| eye injury |
2 points |
| Vascular involvement (thrombophlebitis, deep vein thrombosis, arterial thrombosis, aneurysm) |
1 point |
| Positive pathergy test |
1 point |
| Diagnosed if ≥ 3 positive points |
|