Data |
PCT
n= 60 |
PCT-VIH
n= 21 |
Type of PCT |
f-PCT
n=19 |
s-PCT
n=41 |
s-PCT
n=21 |
Age (years)
Mean value
Range |
31
(7-61) |
50
(27-77) |
41
(26-59) |
Gender |
M |
14 |
24 |
17 |
F |
5 |
17 |
4 |
TUP (mg/24h)
Mean value
Range |
4,655
(765-14,388) |
6,099
(1,250-14,802) |
9,706
(1,464-22,156) |
PPI
Mean value
Range |
5.65
(1.80-10.30) |
4.54
(1.80-8.60) |
6.4
(2.10-9.30) |
f-PCT: Familial PCT; s-PCT: Sporadic PCT; M: male; F: female
Normal values: TUP: Total urinary porphyrins: 20-250 μg/24 h; PPI: Plasma
porphyrin index : ≤ 1.30 |