Clinical Symptoms |
Patient
No. |
Sex |
Age at
onset (year) |
Age at
exam. (year) |
Duration (months
or years) |
CSF cells / protein
/ ul ( /ul, mg/ dl) |
Clinical
course |
Response
to IVIg |
Predominant
symptoms |
Clinical type |
Other symptoms |
1 |
M |
35 |
38 |
3y |
1/135 |
R |
+ |
motor > sensory |
typical CIDP |
double vision, dysarthria |
2 |
M |
39 |
43 |
4y |
2/45 |
R |
+ |
motor ≥ |
sensory typical CIDP |
- |
3 |
F |
33 |
43 |
10y |
2/19 |
R |
+ |
motor >> |
sensory MADSAM |
- |
4 |
F |
74 |
75 |
8m |
7/70 |
CP |
+ |
motor > |
sensory typical CIDP |
- |
5 |
F |
76 |
77 |
1y |
2/66 |
CP |
+ |
motor ≥ |
sensory typical CIDP |
double vision, ptosisb |
6 |
F |
67 |
71 |
4y |
1/29 |
CP |
+ |
motor = |
sensory typical CIDP |
numbness of face |
7 |
M |
75 |
76 |
4m |
0/46 |
R |
+ |
motor > sensory |
MADSAM |
- |
8 |
F |
42 |
42 |
5m |
5/65 |
R |
+ |
motor > sensory |
MADSAM |
double vision, dysarthria ptosis |
9 |
M |
74 |
75 |
5m |
1/49 |
CP |
+ |
motor >> sensory |
typical CIDP |
- |
10 |
M |
65 |
70 |
5 |
1/129 |
CP |
± |
motor = sensory |
typical CIDP |
- |
CP: chronic progressive R: relapsing-remitting
MADSAM: multifocal acquired demyelinating sensory and motor |