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Figure 3: Fundus images of RP1 patients with recessive (A-C) or dominant (D-I) retinitis pigmentosa (see Figure 1 for pedigrees). A: family RP94, left eye of 31 year-old patient II:2, VA (visual acuity) = light perception; B: family RP94, left eye of 29 year-old patient II:4, VA = 0.05; C: family RP494, left eye of 20 year-old patient II:1, VA = 0.30; D: family PHRC115, left eye of 63 year-old patient III:1, VA = no light perception; E: family RP785, left eye of 58 year-old patient II:3, VA = 0.50; F: family PHRC116, left eye of 36 year-old patient III:2, VA = 0.80; G: family RP263, right eye of 58 year-old patient V:1, VA = 0.62; H: family RP785, right eye of 44 year-old patient III:6, VA = 0.62; I: family RP785, left eye of 15 year-old patient IV:2, VA = 1.00. |