| |
Night Blindness |
Visual field defect |
|
Photophobia |
Cataract |
Pigment deposits in fundus |
| |
autosomal recessive retinitis pigmentosa |
| Positive patients/total |
4/4 |
4/4 |
|
4/4 |
2/4 |
4/4 |
| autosomal dominant retinitis pigmentosa |
| Positive patients/total |
14/22 |
15/22 |
14/22 |
|
12/22 |
17/23 |
| |
Age at first exam |
Age at onset |
Visual acuity |
Percentage of
remaining visual field |
Dim blue
scotopic ERG |
White
photopic ERG |
30-Hz flickers
photopic ERG |
| Mean Standard deviation
Range |
autosomal recessive retinitis pigmentosa |
|
|
|
| 10
+1
8-10
n=4 |
5
+8
1-17
n=4 |
0.43*
+0.27
0.18-0.75
n=4 |
45*
+26
16-78
n=4 |
0
n=4 |
0
n=4 |
1
+3
0-5
n=4 |
| Mean Standard deviation
Range |
autosomal dominant retinitis pigmentosa |
|
|
|
| 43
+16
7-64
n=23 |
35
+12
13-51
n=13 |
0.79**
+0.26
0.2-1.25
n=23 |
44**
+28
9-87
n=15 |
91
+88
0-313
n=16 |
47
+39
0-131
n=16 |
38
+31
0-96
n=16 |
