| |
Age |
Sex |
Race |
Symptoms |
Laterality |
Visual acuity |
Location |
Hemorrhage |
RD |
Exudates |
Other system involvement |
Treatment |
Follow-up |
Follow-up outcome |
Family history |
| 1 |
21y |
M |
white |
asymptomatic |
right |
20/20 |
360o of midperipheral |
yes |
no |
no |
cutaneous |
observation |
28m |
unchanged |
no |
| 2 |
25y |
F |
white |
asymptomatic |
right |
20/20 |
360o of midperipheral |
no |
no |
no |
no |
observation |
3y |
unchanged |
no |
| 3 |
9y |
F |
n/a |
acute loss of vision |
right |
6/60 |
macula |
yes |
no |
no |
no |
observation |
1y |
unchanged |
no |
| 4 |
10y |
M |
n/a |
asymptomatic |
right |
20/20 |
superonasal midperipheral |
no |
no |
no |
brain |
observation |
n/a |
unchanged |
yes |
| 5 |
23y |
n/a |
n/a |
asymptomatic |
unilateral |
n/a |
n/a |
no |
no |
no |
brain |
laser |
33y |
slowly increased |
no |
| 6 |
16y |
M |
caucasian |
asymptomatic |
left |
20/20 |
inferiorly |
no |
no |
no |
cutaneous |
observation |
7y |
unchanged |
yes |
| 7 |
44y |
F |
white |
asymptomatic |
bilateral |
20/20 |
optic disc superiotemporal |
yes |
no |
no |
brain |
observation |
n/a |
unchanged |
yes |
| 8 |
17y |
F |
n/a |
asymptomatic |
left |
20/20 |
optic disc |
no |
no |
no |
no |
observation |
1.5y |
unchanged |
no |
| 9 |
13y |
M |
n/a |
strabismus and decreased vison |
right |
6/60 |
superonasal |
no |
no |
no |
no |
observation |
1.5y |
unchanged |
no |
| 10 |
6y |
M |
n/a |
esotropia |
right |
20/30 |
optic disc |
yes |
no |
no |
no |
observation |
5y |
larger |
no |
| 11 |
74y |
F |
n/a |
decreased vision |
right |
20/25 |
optic disc |
yes |
no |
no |
no |
vitrectomy |
30y |
increase in numbers |
no |
| 12 |
38y |
M |
n/a |
decreased vision |
right |
CF |
optic nerve |
yes |
no |
no |
no |
vitrectomy |
7y |
VA improved |
no |
| 13 |
35y |
M |
n/a |
decrease vision and pain |
right |
LP |
optic nerve |
yes |
no |
no |
no |
enucleation |
n/a |
unchanged |
no |
| 14 |
38y |
M |
n/a |
n/a |
right |
n/a |
inferior temporal |
n/a |
n/a |
no |
no |
n/a |
n/a |
n/a |
yes |
| 15 |
13y |
F |
white |
asymptomatic |
right |
20/20 |
superiotemporal |
no |
no |
no |
no |
observation |
n/a |
n/a |
no |
| 16 |
9y |
M |
white |
seizures |
right |
20/20 |
optic disc |
no |
no |
no |
brain |
observation |
n/a |
n/a |
yes |
| 17 |
14y |
F |
white |
headaches |
left |
20/20 |
peripheral retina |
no |
no |
no |
brainstem |
observation |
n/a |
n/a |
yes |
| 18 |
22y |
F |
n/a |
asymptomatic |
left |
20/20 |
nasally |
yes |
no |
no |
n/a |
photocoagulation |
4y |
hemorrhage |
no |
| 19 |
28y |
F |
n/a |
asymptomatic |
right |
20/20 |
superior |
no |
no |
n/a |
no |
n/a |
n/a |
n/a |
no |
| 20 |
13y |
M |
n/a |
asymptomatic |
bilateral |
20/20 |
n/a |
no |
no |
np |
no |
observation |
4y |
unchanged |
yes |
| 21 |
10y |
F |
n/a |
asymptomatic |
right |
20/20 |
midperiphery |
no |
no |
no |
brain |
observation |
16y |
increased fibrous tissue |
yes |
| 22 |
8y |
F |
n/a |
asymptomatic |
left |
20/20 |
n/a |
no |
no |
no |
no |
observation |
n/a |
n/a |
yes |
| 23 |
43y |
F |
n/a |
decreased vision |
right |
1/10 |
macula |
no |
no |
no |
no |
obs |
n/a |
n/a |
no |
| 24 |
18y |
M |
n/a |
Squint
poor vision |
left |
CF |
macula
inferotemporal |
no |
no |
no |
no |
observation |
n/a |
n/a |
no |
| 25 |
32y |
M |
n/a |
transient visual disturbance |
right |
20/20 |
inferior |
no |
no |
no |
cutaneous
brain |
observation |
n/a |
n/a |
yes |
| 26 |
55y |
F |
n/a |
asymptomatic |
left |
20/20 |
n/a |
n/a |
n/a |
n/a |
n/a |
n/a |
n/a |
n/a |
n/a |
| 27 |
14y |
M |
n/a |
asymptomatic |
right |
20/20 |
nasal |
no |
no |
no |
no |
observation |
15y |
aneurysm occlusion |
n/a |
| 28 |
3y |
F |
n/a |
asymptomatic |
left |
20/400 |
n/a |
n/a |
n/a |
n/a |
n/a |
n/a |
n/a |
n/a |
n/a |
| 29 |
23y |
F |
n/a |
decrease vision |
right |
20/100 |
macula |
n/a |
n/a |
n/a |
n/a |
n/a |
n/a |
n/a |
n/a |
| 30 |
50y |
M |
n/a |
asymptomatic |
left |
20/20 |
n/a |
n/a |
n/a |
n/a |
n/a |
n/a |
n/a |
n/a |
n/a |
| 31 |
10y |
M |
n/a |
asymptomatic |
left |
20/20 |
n/a |
n/a |
n/a |
n/a |
n/a |
n/a |
n/a |
n/a |
n/a |
| 32 |
1y |
F |
n/a |
asymptomatic |
right |
normal |
superior nasal |
no |
no |
no |
no |
observation |
1y |
unchanged |
no |
| 33 |
12y |
M |
n/a |
decreased vision |
left |
20/100 |
inferotemporal |
no |
no |
no |
no |
observation |
2y |
unchanged |
no |
| 34 |
18y |
F |
n/a |
decreased vision |
right |
20/50 |
throughout the fundus |
no |
no |
no |
no |
observation |
1y |
unchanged |
no |
| 35 |
6-month |
F |
n/a |
white pupillary reflex |
left |
NLP |
n/a |
no |
yes |
yes |
no |
enucleation |
n/a |
n/a |
no |
| 36 |
37y |
M |
n/a |
decreased vision |
right |
CF |
inferior |
yes |
no |
no |
no |
observation |
6y |
improved |
no |
| 37 |
44y |
F |
white |
decreased vision |
left |
4/10 |
macula |
no |
no |
no |
no |
obs |
n/a |
n/a |
no |
| 38 |
4-month |
M |
n/a |
skin lesion |
left |
n/a |
macula |
yes |
no |
no |
cutaneous |
observation |
2y |
epithelial defect |
no |
| 39 |
25y |
M |
white |
asymptomatic |
left |
20/20 |
optic disc |
no |
no |
no |
no |
observation |
n/a |
n/a |
no |
| 40 |
16y |
F |
n/a |
asymptomatic |
right |
20/20 |
temporal |
yes |
no |
no |
no |
observation |
21y |
vitrous hemorrage |
no |
| 41 |
27y |
M |
n/a |
asymptomatic |
left |
20/20 |
temporal |
no |
no |
no |
no |
observation |
n/a |
n/a |
no |
| 42 |
26y |
M |
n/a |
asymptomatic |
bilateral |
20/20 |
temporal |
no |
no |
no |
cutaneous |
observation |
8y |
unchanged |
yes |
| 43 |
16y |
M |
n/a |
asymptomatic |
right |
20/20 |
peripheral |
no |
no |
no |
no |
observation |
6y |
Increased
fibrous tissue |
no |
| 44 |
70y |
M |
n/a |
grand mal |
left |
normal |
peripheral |
no |
no |
no |
no |
observation |
n/a |
n/a |
yes |
| 45 |
10y |
M |
n/a |
astigmatism |
right |
0.4 |
peripheral |
no |
no |
no |
no |
observation |
2y |
unchanged |
no |
| 46 |
4y |
F |
n/a |
asymptomatic |
right |
normal |
nasal peripheral |
no |
no |
no |
no |
observation |
1y |
unchanged |
no |
| 47 |
39y |
F |
n/a |
diplopia |
right |
20/20 |
superonasal |
no |
no |
no |
cutaneous
brain |
observation |
2y |
unchanged |
yes |
| 48 |
10y |
F |
n/a |
asymptomatic |
bilateral |
20/20 |
inferonasal superotemporal |
no |
no |
no |
no |
observation |
4y |
unchanged |
yes |
| 49 |
10y |
F |
white |
asymptomatic |
left |
20/20 |
superotemporal |
no |
no |
no |
n/a |
observation |
n/a |
n/a |
no |
| 50 |
18y |
F |
white |
asymptomatic |
left |
1/20 |
optic nerve |
no |
no |
no |
no |
observation |
n/a |
n/a |
no |
| 51 |
7y |
F |
white |
decreased vision |
left |
1/20 |
macula |
no |
no |
no |
no |
observation |
n/a |
n/a |
no |
| 52 |
37y |
n/a |
white |
diplopia |
right |
20/20 |
inferior |
no |
no |
no |
no |
observation |
n/a |
n/a |
no |
| 53 |
40y |
n/a |
white |
decreased vision |
left |
9/10 |
superotemporal |
no |
no |
no |
no |
observation |
n/a |
n/a |
no |
| 54 |
63y |
n/a |
white |
asymptomatic |
right |
20/20 |
inferior |
no |
no |
no |
no |
obs |
n/a |
n/a |
no |
| 55 |
25y |
n/a |
white |
asymptomatic |
right |
20/20 |
temperal |
no |
no |
no |
no |
obs |
n/a |
n/a |
no |
| 56 |
19y |
M |
white |
decreased vision |
right |
6/10 |
nasal |
no |
no |
no |
no |
obs |
n/a |
n/a |
no |
| 57 |
48y |
M |
white |
asymptomatic |
right |
20/20 |
superonasal |
no |
no |
no |
cutaneous
brain |
observation |
5y |
unchanged |
no |
| 58 |
19y |
M |
white |
asymptomatic |
left |
14/21 |
superior |
no |
no |
no |
brain |
observation |
5y |
aneurysm occlusion |
no |
| 59 |
50y |
M |
black |
decreased vision |
left |
20/200 |
macula |
no |
no |
no |
no |
observation |
n/a |
n/a |
no |
| 60 |
71y |
M |
white |
reading discomfort |
right |
20/30 |
temporal |
yes |
no |
no |
no |
photocoagulate |
5 m |
unchanged |
no |
| 61 |
19y |
M |
white |
asymptomatic |
left |
20/20 |
temporal |
no |
no |
no |
no |
photocoagulation |
5y |
subretinal hemorrhage |
no |
| 62 |
53y |
M |
white |
poor vision |
right |
HM |
inferior |
yes |
no |
no |
no |
no |
n/a |
n/a |
no |
| 63 |
8y |
F |
n/a |
asymptomatic |
n/a |
n/a |
n/a |
no |
no |
no |
no |
observation |
7y |
slightly changed |
no |
| 64 |
63y |
M |
white |
asymptomatic |
right |
20/30 |
temporal |
no |
no |
no |
no |
observation |
34y |
slightly
changed |
no |
| 65 |
35y |
M |
black |
asymptomatic |
right |
20/20 |
inferotemporal |
no |
no |
no |
no |
observation |
3y |
unchanged |
no |
| 66 |
45y |
F |
white |
asymptomatic |
right |
20/15 |
nasal |
no |
no |
no |
no |
observation |
n/a |
n/a |
n/a |
| 67 |
37y |
F |
white |
blurred vision
strabismus |
left |
0.1 |
macula temporal |
yes |
yes |
no |
no |
observation |
13y |
slight changed |
no |
| 68 |
2.5y |
F |
white |
esotropia |
right |
n/a |
superotemporal |
yes |
yes |
no |
no |
photocoagulation |
4.5y |
hemorrhage |
no |
| 69 |
33y |
F |
white |
asymptomatic |
right |
20/20 |
inferior nasal |
no |
no |
no |
cutaneous |
observation |
5y |
aneurysm occlusion |
yes |
| 70 |
51y |
F |
white |
asymptomatic |
right |
20/15 |
optic nerve |
no |
no |
no |
no |
observation |
6y |
unchanged |
no |
| 71 |
21y |
F |
white |
decreased vision |
right |
20/30 |
temporal |
no |
no |
no |
cutaneous
brain |
observation |
4y |
unchanged |
no |
| 72 |
47y |
F |
n/a |
decrease vision |
left |
n/a |
n/a |
yes |
no |
no |
no |
photocoagulation |
10y |
hemorrhage absorbed |
no |
| 73 |
13y |
M |
white |
keratitis |
bilateral |
20/20 |
peripheral |
no |
no |
no |
no |
observation |
2y |
increased in numbers |
yes |
| 74 |
10y |
F |
white |
asymptomatic |
right |
20/20 |
superotemporal |
no |
no |
no |
no |
observation |
n/a |
n/a |
yes |
| 75 |
24y |
F |
n/a |
asymptomatic |
bilateral |
n/a |
inferior |
no |
no |
no |
no |
n/a |
n/a |
n/a |
n/a |
| 76 |
14y |
M |
n/a |
asymptomatic |
left |
normal |
optic nerve |
yes |
no |
no |
n/a |
n/a |
n/a |
n/a |
n/a |
| 77 |
2y |
F |
white |
n/a |
n/a |
n/a |
midperiphery |
yes |
no |
no |
n/a |
enucleate |
n/a |
n/a |
n/a |
| 78 |
34y |
M |
white |
decreased vision |
right |
n/a |
optic nerve |
n/a |
n/a |
n/a |
no |
n/a |
n/a |
n/a |
n/a |
| 79 |
26y |
F |
white |
routine refraction |
left |
20/20 |
n/a |
yes |
yes |
no |
cutaneous |
n/a |
n/a |
n/a |
n/a |
| 80 |
11y |
F |
n/a |
decreased vision |
right |
5/100 |
macula |
no |
no |
no |
n/a |
n/a |
n/a |
n/a |
n/a |
| 81 |
4y |
M |
n/a |
decreased vision,esotropia |
left |
3/200 |
nasal |
yes |
no |
no |
n/a |
n/a |
n/a |
n/a |
n/a |
| 82 |
54y |
M |
n/a |
retrobulbar pain |
left |
20/20 |
n/a |
n/a |
n/a |
n/a |
cutaneous |
enucleation |
n/a |
n/a |
n/a |
| 83 |
7y |
F |
n/a |
asymptomatic |
left |
20/20 |
n/a |
n/a |
n/a |
n/a |
n/a |
n/a |
n/a |
n/a |
n/a |
| 84 |
17y |
F |
n/a |
headaches |
unilateral |
n/a |
superotemporal |
no |
n/a |
no |
cutaneous
brain |
n/a |
n/a |
n/a |
yes |
| 85 |
21y |
M |
n/a |
headaches
decreased vision |
bilateral |
15/400 |
n/a |
no |
no |
no |
no |
observation |
7 m |
unchanged |
n/a |
| 86 |
32y |
M |
n/a |
mild decreased vision |
right |
n/a |
optic nerve |
yes |
yes |
n/a |
no |
n/a |
n/a |
n/a |
n/a |
| 87 |
11y |
F |
asian |
asymptomatic |
right |
20/200 |
inferotemporal |
no |
no |
no |
no |
observation |
5 y |
unchanged |
no |
| 88 |
19y |
F |
n/a |
Decreased vision and floaters |
left |
20/20 |
superotemporal |
yes |
no |
no |
no |
observation |
5 m |
improved |
no |
| 89 |
63y |
M |
n/a |
Decreased vision |
right |
20/400 |
macula |
no |
no |
no |
no |
infliximab |
6 m |
improved |
no |
| 90 |
0d |
F |
white |
hyphema |
left |
n/a |
inferior |
yes |
n/a |
no |
no |
enucleation |
52 y |
n/a |
no |
| 91 |
18y |
M |
mestizo |
scotoma |
Right |
n/a |
inferotemporal |
no |
no |
no |
n/a |
observation |
48 m |
unchanged |
n/a |
| 92 |
43y |
M |
n/a |
asymptomatic |
left |
20/30 |
supertemporal |
n/a |
n/a |
n/a |
no |
n/a |
n/a |
n/a |
no |
| 93 |
28y |
F |
n/a |
asymptomatic |
right |
20/30 |
inferior |
yes |
n/a |
n/a |
no |
n/a |
n/a |
n/a |
no |
| 94 |
29y |
F |
n/a |
paracentral |
right |
20/20 |
Optic disc |
yes |
n/a |
n/a |
no |
n/a |
1 m |
hemorrhage absorbed |
n/a |
| 95 |
12y |
F |
n/a |
asymptomatic |
right |
6/6 |
nasal |
n/a |
n/a |
n/a |
n/a |
n/a |
n/a |
n/a |
n/a |
| 96 |
30y |
F |
n/a |
asymptomatic |
right |
20/20 |
macula |
yes |
n/a |
n/a |
brain |
n/a |
n/a |
n/a |
yes |
