Groups BNP
[pg/ml]
NT-proBNP
[pg/ml]
ANP
[pg/ml]
NT-proANP
[nmol/l]
AD-EDMD 42 (18-54) *,# 85 (17-195) * 273 (1.3-366) 0.50 (0.28-0.58) ##
X-EDMD 24 (6-105) # 53 (14-192) 366 (0.9-391) 0.54 (0.37-0.60) ##
X-EDMD carriers 22 (9-62) 87 (33-400) 8.1 (0.9-8.1) 0.34 (0.29-0.65)
Dystrophinopathies 163 (50-337) *** 103 (9-457) * 344 (286-362) *** 2.5 (1.6-2.6) ***
Healthy controls 15 (9-20) 29 (15-49) 4.9 (2.3-5.6) 0.38 (0.32-0.42)
Medians and interquartile ranges are presented
* p<0.05, ** p<0.005, *** p<0.0005 for the patient groups vs. healthy controls
# p<0.05, ## p<0.005; AD-EDMD or X-EDMD patients vs. disease controls
Table 2: Natriuretic peptide concentrations in EDMD patients and controls