| Lead Author |
Year |
Patients |
Outcomes |
| Lundstrom[83] |
1990 |
111 patients from Hospital for Sick Children and National Heart Hospital of whom51 underwent surgery |
Operative mortality: 11/51 (22%)
Dilated systemic ventricle is a risk factor for a poor outcome
|
| Termignon[79] |
1996 |
52 patients from Laennec Hospital, Paris |
Operative mortality: 15%
Survival: 83% at 1 year, 55% at 10 years (for patients with associated VSD/LVOTO) while those with only associated VSD had 71% survival at 10 years
|
| Van Son [80] |
1995 |
40 patients from Mayo Clinic |
Operative mortality 10%
Survival: 78% at 5 years, 61% at 10 years
RVEF > 44% favored survival
|
| Yeh[81] |
1999 |
127 patients underwent surgery at Hospital for Sick Children,median age at operation was8 years |
Operative mortality 6%
Survival: 48% at 20 years
|
| Hraska[82] |
2005 |
123 patients underwent surgery at Children’s Hospital Boston, median age at operation was 7.9 years |
Survival: 84% at 1 year, 75% at 5 years; 68% at 10 years, and 61% at 15 years
Freedom from RV dysfunction (2V repair) 43% at 15 years
Ebstein malformation of the tricuspid valve is a risk factor for RV dysfunction
|
