1. Prenatal Or Developmental Pulmonary Hypertensive Vascular Disease.
1.1. Associated with Maternal or Placental Abnormalities: chorioamnionitis, preeclampsia,…
1.2. Associated with Fetal Pulmonary Vascular Maldevelopment: congenital alveolar dysplasia,..
1.3. Associated with Cardiac Fetal Maldevelopment: premature closure of PDA/F.ovale, obstructed TAPVR
2. Perinatal Pulmonary Vascular Maladaptation (PPHN)
2.1. Idiopathic PPHN.
2.2. Associated with or triggered by: sepsis, meconium, CHD, diaphragmatic hernia trisomies,diazoxide,..
3. Pediatric Cardiovascular Disease
3.1. Systemic to Pulmonary shunts.
3.2. Postoperative PAH After Shunts Closure, Repair of D-TGA, Fallot, Left Heart Obstruction,…
3.3. Pulmonary Vascular Disease following Staged Palliation For Single Ventricle Physiology.
3.4. PVD Associated with Congenital Abnormalities of Pulmonary Arteries or Veins.
3.5. Pulmonary Venous Hypertension
4. Bronchopulmonary Dysplasia
4.1. Associated with Pulmonary Vascular Hypoplasia.
4.2. Associated with Pulmonary Vein Stenosis.
4.3. Associated with Left Ventricular Diastolic Dysfunction.
4.4. Associated with Systemic to Pulmonary shunts (PDA, ASD, VSD, aorto pulmonary collaterals).
4.5. Associated with Significant Hypercabia and/or Hipoxia.
5. Isolated Pediatric Pulmonary Hypertensive Vascular Disease.
5.1. Idiopathic.
5.2. Heritable.
5.3. Drugs and toxins
5.4. Pulmonary Veno-occlusive Disease and Pulmonary Capillary Hemangiomatosis
6. Multifactorial PVD in Congenital Malformation Syndromes.
6.1. With Associated Congenital Heart Disease.
6.2. Without Associated Congenital Heart Disease.
7. Pediatric Lung Disease: Cystic fibrosis, interstitial lung disease, sleep disordered breathing
8. Pediatric Thromboembolic Disease.
9. Pediatric Hypobaric Hypoxic Exposure.
10. Pediatric Pulmonary Vascular Disease Associated With Other System Disorders: portal hypertension, hematological, oncological, metabolic, autoimmune disorders…      
Table 2: Classification of pediatric Pulmonary Hypertensive Vascular Disease (PHVD) - Panamá Classification 2011. Abbreviated schema according to (3).