Author Year Totalpatients Overlappatients Prevalence Diagnosticcriteria† Boberg et al. [82] 1996 114 with PSC 2 definite 38 probable 2% 33% Original scoring system Czaja [2] 1998 162 with AIH 0 0% Modified IAIHG scoring system 26 with PSC 14 54% Van Buuren et al. [76] 2000 113 with PSC 9 8% Descriptive 9 definite 0 probable 8% Original scoring system 8 definite 1 probable 7% 1% Revised scoring system Kaya et al. [81] 2000 211 with PSC 4 definite 40 probable 2% 19% Original scoring system 3 definite 13 probable 1% 6% Revised scoring system Gheorghe et al. [48] 2004 82 with AIH 6 7% Revised scoring system/descriptive PSC Floreani et al. [90] 2005 41 with PSC 7 17% Revised scoring system/Descriptive PSCand ERCP Czaja [46] 2008 24 with PSC 2 definite 7 probable 8% 29% Revised scoring system 2 definite 3 probable 8% 13% Simplified scoring system Chandok et al. [91] 2010 147 with PSC 0 definite 0 probable   0% Revised scoring system 0 definite 2 probable 0% 1% Simplified scoring system Hunter et al. [92] 2011 118 with AIH 12* 10% Descriptive AIH/PSC cholestasis andMRC Notes:* identified from 24 patients with cholestasis; †please see references for details on diagnostic criteria.

Table 5: Large studies reporting prevalence of AIH-PSC overlap syndrome.