Pt no. Age at Diagnosis* Sex Ethnicity Attack Frequency Current Treatment Regimen MGUS
1 45 M C Every 4-6 weeks IVIG IgG kappa
2 49 F C Weekly/monthly IVIG IgG kappa
3 45 M C Every weekend Infliximab IgG kappa
4 55 M C > 2/yr IVIG IgG kappa
5 46 F C 5-10 day intervals N/A (deceased) IgG lambda
6 42 M C 3-4 year intervals Theophylline IgG kappa
7 32 M C 3-5 year intervals IVIG IgG kappa
8 59 M C Single episode None IgG kappa
9 65 M C 3-4/year IVIG IgG kappa
10 39 F C Chronic T/T** ND#
11 48 F C Infrequent T/T IgG lambda
12 48 M C weekly IVIG IgG kappa
13 50 F C > 2x/yr IVIG IgG kappa
14 51 M C > 2x/yr IVIG IgG
15 53 M C Weekly IVIG IgG lambda
16 40 F C Chronic Theophylline IgG kappa
17 43 F C 3-4 year interval None IgG kappa
18 64 F C Chronic Theophylline IgG kappa
19 48 M AA 3-4/yr IVIG IgG lambda
20 43 M C Bimonthly IVIG IgG kappa
21 65 M C Single episode Theophylline IgG kappa
22 43 M C < 2x/yr IVIG IgG kappa
23 36 F C < 2x/yr IVIG IgG kappa
24 66 M C < 2x/yr IVIG IgG lambda
25 40 F C Single episode IVIG IgG kappa
26 62 M C < 2x/yr IVIG IgG kappa
27 7 F C Chronic plus acute Subcutaneous IG ND#
28 48 M C < 2x/yr IVIG IgG lambda
29 61 M C 3-4 year intervals IVIG IgG kappa
30 43 F C < 2x/yr IVIG IgG lambda
31 58 F C Chronic plus acute None IgM kappa
32 33 M C < 2x/yr IVIG ND#
33 37 F C Chronic plus acute IVIG ND#
34 22 mo. F C Every 5-6 months   ND#
35 8 C C Weekly IVIG ND#
*Note: Many patients experienced episodes consistent with SCLS prior to formal diagnosis; **: Theophylline plus terbutaline; #:  Not detected
Table 1: Clinical profiles of SCLS subjects.