Neonatal Persistent pulmonary hypertension, respiratory distress syndrome, chronic lung disease
Cardiac Left to right shunt (ASD, VSD, AVSD, PA), Transposition of the great arteries, obstructive lesions (TAPVC, MS, HLHS, HOCM, DCM)
Acquired Chronic hypoxia (Cystic fibrosis, high altitude), scoliosis, airway obstruction (OSA, tonsillar hypertrophy, tracheal stenosis), vasculitic (uncommon- connective tissue disease, sickle cell)
Idiopathic Sporadic, familial
ASD, atrial septal defect; AVSD atrioventricularseptal defect; DCM, dilated cardiomyopathy; HLHS, hypoplastic left heart syndrome; HOCM, hypertrophic obstructed cardiomyopathy; MS, mitral stenosis; OSA, obstructive sleep apnoea; PA, pulmonary arterial; TAPVC, total anomalous pulmonary venous connection; VSD, ventricular septal defect
Table 1: Causes of PAH in paediatrics. Adapted from Tulloh, 2005 [5].