Familial Mediterranean fever (FMF) Urate crystal arthritis (gout)
Familial cold autoinflammatory syndrome (FCAS) Behçet’s syndrome
TNF receptor-associated periodic syndrome (TRAPS) Pericarditis
Neonatal-onset multi-inflammatory disease (NOMID) PAPA syndrome
Deficiency of the interleukin-1–receptor antagonist (DIRA) Blau’s syndrome
Muckle-Wells syndrome (MWS) Sweet’s syndrome
Normocomplementemic urticarial vasculitis Type 2 diabetes
Hyper IgD syndrome (HIDS) Majeed syndrome
Chronic recurrent multifocal osteomyelitis (CRMO) Cherubism
Systemic-onset juvenile idiopathic arthritis (soJIA) FCAS2
Mevalonic aciduria Early-onset enterocolitis (IBD)
Macrophage activation syndrome (MAS) Anti-synthetase syndrome
Schnitzler’s syndrome Adult-onset Still’s disease
The family of autoinflammatory diseases
Table 1: Autoinflammatory diseases.