Insufficient level of evidence for the treatment of major vascular involvement |
No controlled trial demonstrated no benefit of anticoagulants, antiplatelet, fibrinolytic in venous or arterial thrombosis |
Deep vein thrombosis (DVT):
immunosuppressive
- Azathioprine
- Cyclophosphamide
- Corticosteroids
- Cyclosporine A |
Risk of fatal hemorrhage when associated aneurysm
Response to immunosuppressive |
arterial aneurysms
- Cyclophosphamide
- And corticosteroids |
No preventive effect of recurrences |