Insufficient level of evidence for the treatment of major vascular involvement No controlled trial demonstrated no benefit of anticoagulants, antiplatelet, fibrinolytic in venous or arterial thrombosis
Deep vein thrombosis (DVT):
- Azathioprine
- Cyclophosphamide
- Corticosteroids
- Cyclosporine A
Risk of fatal hemorrhage when associated aneurysm
Response to immunosuppressive
arterial aneurysms
- Cyclophosphamide
- And corticosteroids
No preventive effect of recurrences
Table 4: Dependent therapeutic recommendations lesion site