Prostacyclin analogues Epoprostenol (iv) Treprostinil (sc/iv/inhaled) Iloprost (inhaled) Endothelin receptor antagonists Bosentan (po) Ambrisentan (po) Phosphodiesterase type 5 inhibitors Sildenafil (po) Tawdalafil (po) Nitric oxide (inhaled)

Table 4: Drugs for treatment of PAH when vasoreactivity test is negative.