Prostacyclin analogues
Epoprostenol (iv)
Treprostinil (sc/iv/inhaled)
Iloprost (inhaled)
Endothelin receptor antagonists
Bosentan (po)
Ambrisentan (po)
Phosphodiesterase type 5 inhibitors
Sildenafil (po)
Tawdalafil (po)
Nitric oxide (inhaled)
Table 4:
Drugs for treatment of PAH when vasoreactivity test is negative.