Pulmonary atresia is a heart defect present at birth (congenital) that's normally diagnosed within the first few hours or days of life. In pulmonary atresia, the valve that lets blood out of the heart to go to your baby's lungs doesn't form correctly. Instead of opening and closing to allow blood to travel from your heart to your lungs, a solid sheet of tissue forms. Blood from the right side of your baby's heart can't go back to the lungs to pick up oxygen.Pulmonary atresia may occur with or without a ventricular septal defect (VSD).
Bluish colored skin (cyanosis), Fast breathing, Fatigue, Poor eating habits (babies may get tired while nursing or sweat during feedings), Shortness of breath.The temporary measure, which has to be taken in new-borns with pulmonary atresia, is usually given an intravenous drug (injected into a vein) called prostaglandin E1 to prevent the ductus arteriosus from closing. Blood can flow from the right side of the heart to the left side and pass through the left ventricle to the lungs to pick up oxygen by keeping the ductus arteriosus open. Cardiac catheterization is used to diagnose heart problems, It can also be used to enlarge the opening in the septum.
In Finland, the analysis on pulmonary atresia got the result as almost one-quarter of the cohort died (nâ??=â??932 deaths) and, of these, 727 (78%) deaths occurred within the first year and 323 (35%) within the first month of life. Although the risk of death was lower after the first year of life, 20% of all cohort deaths occurred after one year of age. Death occurred before intervention, or parents chose palliative care, for 144 (4%) children who died without any procedure; most of these children had hypo-plastic left heart and/or mitral atresia (HLH/MA).