Eisenmenger syndrome is a condition that affects blood flow from the heart to the lungs in some people who were born with structural problems of the heart. Eisenmenger syndrome is a condition that results from abnormal blood circulation caused by a defect in the heart. Most often, people with this condition are born with a hole between the two pumping chambers -- the left and right ventricles -- of the heart (ventricular septal defect). The hole allows blood that has already picked up oxygen from the lungs to flow back into the lungs, instead of going out to the rest of the body.
Bluish lips, fingers, toes, and skin (cyanosis) Chest pain Coughing up blood Dizziness Fainting Feeling tired Shortness of breath Stroke Swelling in the joints caused by too much uric acid (gout)
Complete blood count (CBC) Chest x-ray MRI scan of the heart Putting a thin tube in an artery to view the heart and blood vessels and measure pressures (cardiac catheterization) Test of the electrical activity in the heart (electrocardiogram) Ultrasound of the heart (echocardiogram)
Medications: include calcium channel blockers, prostacyclin, and endothelin receptor antagonists, Oxygen: Supplemental oxygen may be used during sleep periods or while resting. Use of oxygen may progress to continuous use for symptom relief. Phlebotomy: (removal of blood) should not be done frequently, but may be recommended when erythrocytosis causes hyperviscosity (extreme thickness) of the blood. Phlebotomy is generally done only when symptoms are severe and/or the hematocrit (the percentage of blood that is made up of red blood cells) becomes extremely elevated.