Pulmonary atresia is a heart defect present at birth (congenital) that's normally diagnosed within the first few hours or days of life. In pulmonary atresia, the valve that lets blood out of the heart to go to your baby's lungs doesn't form correctly. Instead of opening and closing to allow blood to travel from your heart to your lungs, a solid sheet of tissue forms. Blood from the right side of your baby's heart can't go back to the lungs to pick up oxygen.Pulmonary atresia may occur with or without a ventricular septal defect (VSD).
Bluish colored skin (cyanosis), Fast breathing, Fatigue, Poor eating habits (babies may get tired while nursing or sweat during feedings), Shortness of breath.he temporary measure, which has to be taken in new-borns with pulmonary atresia, is usually given an intravenous drug (injected into a vein) called prostaglandin E1 to prevent the ductus arteriosus from closing. Blood can flow from the right side of the heart to the left side and pass through the left ventricle to the lungs to pick up oxygen by keeping the ductus arteriosus open.
Statistical Analysis of pulmonary atresia in india got the results as in 124 patients between 1997 and 2010, median sternotomy approach was used in 116 patients, and clamshell approach was used in 8 patients. All the patients had a single-stage complete unifocalization, of whom 60% (n=74) had final repair (VSD closure and RV-to-pulmonary artery conduit), 21% (n=26) had an RV-to-pulmonary artery conduit alone (VSD left open), and 19% (n=24) had a central shunt. Tissue-to-tissue anastomosis was achieved in most of the patients In 10 patients, homograft tissue was used for augmentation and in one patient, a 14-mm PTFE tube graft was used to achieve the confluence of the pulmonary arteries.