Anesthetic Considerations in Pediatric Patients with Epidermolysis Bullosa: A Case Report
Sung-Mi Ji, Sung-Man Hong, Chae-Min Cho, Min-A Kwon and Seok-kon Kim*
Department of Anesthesiology and Pain Medicine, College of Medicine, Dankook University, Cheonan, Korea
- *Corresponding Author:
- Seok-kon Kim
Department of Anesthesiology and Pain Medicine
College of Medicine, Dankook University, Cheonan, Korea
E-mail: [email protected]
Received date: June 06, 2017; Accepted date: June 21, 2017; Published date: June 23, 2017
Citation: Ji SM, Hong SM, Cho CM, Kwon MA, Kim SK (2017) Anesthetic Considerations in Pediatric Patients with Epidermolysis Bullosa: A Case Report. J Anesth Clin Res 8:735. doi: 10.4172/2155-6148.1000735
Copyright: © 2017 Ji SM, et al. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.
Epidermolysis bullosa (EB), a rare genetic disorder with abnormal fragility of skin and mucous membranes, is characterized by blister formation, either spontaneously or following a minor friction. In addition to the skin, it often involves other epithelial-lined organs requiring profound considerations in the anesthetic management related to some comorbidities. Monitoring, difficult airway, positioning, nutritional deficiencies and poor immunity can be challenging for the anesthesiologist in perioperative management. The authers described an experience of a 3-year-old male child with a dystrophic type of EB since birth who underwent hernioplasty. Perioperative careful management and minimal mandatory monitoring might be needed to minimize mechanical injury to the skin and mucous membranes.