alexa De Bukes Syndrome - Tetrology of Fallot with Absent Left Pulmonary Artery | OMICS International| Abstract

Cardiovascular Therapy: Open Access

  • Case Report   
  • Cardiovasc Ther 2016, Vol 1(1): 105

De Bukes Syndrome - Tetrology of Fallot with Absent Left Pulmonary Artery

Madhu KJ*, Sunil Kumar, Vijayalakshmi IB, Chitra and Manjunath CN
Department of Cardiology, Sri Jayadeva Institute of Cardiovascular Sciences and Research, India
*Corresponding Author : Madhu KJ, Department of Cardiology, Sri Jayadeva Institute of Cardiovascular Sciences and Research, India, Tel: +9902783016, Email: [email protected]

Received Date: Jan 25, 2016 / Accepted Date: Feb 26, 2016 / Published Date: Jan 03, 1970

Abstract

De Bucket syndrome - TOF with unilateral absence of a pulmonary artery (UAPA) is a rare condition with an estimated prevalence of 1 in 200,000 young adults. Most commonly, UAPA occurs in conjunction with cardiovascular abnormalities such as tetralogy of Fallot (TOF) coarctation of the aorta, VSD, subvalvular aortic stenosis, transposition of the great arteries (plus VSD or pulmonary stenosis), Taussig-Bing malformation and coarctation, congenitally corrected transposition and pulmonary stenosis, scimitar syndrome. Patients with isolated UAPA can remain asymptomatic into late adulthood but usually report symptoms such as dyspnea or chest pain or suffer from hemoptysis or recurrent infections. Diagnosis can be difficult due to the rarity of the condition and its nonspecific presentation. We present a case of a 5month old child who presented with TOF with Right pulmonary artery stenosis and absent left pulmonary artery, with typical findings on chest radiograph, angiographic features and treatment discussed.

Keywords: Tetrology of fallot; Right pulmonary artery; Left pulmonary artery; Balloon dilatation

Citation: Madhu KJ, Kumar S, Vijayalakshmi IB, Chitra Manjunath CN (2016) De Bukes Syndrome - Tetrology of Fallot with Absent Left Pulmonary Artery. Cardiovasc Ther 1: 105.

Copyright: © 2016 Madhu KJ, et al. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.

Select your language of interest to view the total content in your interested language

Post Your Comment
Share This Article
Recommended Conferences
  • Cardiology Meeting 2018

    June 25-26, 2018 Kuala Lumpur, Malaysia

  • Clinical & Medical Case Reports in Cardiology

    July 05-06, 2018 Berlin, Germany

  • Cardiovascular Imaging

    July 11-12, 2018 Sydney,Australia

  • Cardiology and Cardiovascular Pharmacology

    October 20-21, 2018 Osaka, Japan

Viewmore
Article Usage
  • Total views: 9183
  • [From(publication date): 2-2016 - Jun 20, 2018]
  • Breakdown by view type
  • HTML page views: 9040
  • PDF downloads: 143
Leave Your Message 24x7