Herlyn-Werner-Wunderlich Syndrome /OHVIRA Syndrome; A Rare Urogenital Anomaly with Unusual Presentation in Two Cases with Review of Literature
Kamal Singh*, Sita Thakur, Anjali Soni and Ashok Verma
Department of Obstetrics and Gynaecology, Dr Rajender Prasad Govt Medical College Kangra at Tanda, Himachal Pradesh, India
- Corresponding Author:
- Kamal Singh
Department of Obstetrics and Gynaecology
Dr Rajender Prasad Govt Medical College
Kangra at Tanda, Himachal Pradesh, India
Tel: +91 9418033627
E-mail: [email protected]
Received Date: January 18, 2016 Accepted Date: January 28, 2016 Published Date: February 27, 2016
Citation: Singh K, Thakur S, Soni A, Verma A (2016) Herlyn-Werner-Wunderlich Syndrome /OHVIRA Syndrome; A Rare Urogenital Anomaly with Unusual Presentation in Two Cases with Review of Literature. Clinics Mother Child Health 13:222. doi:10.4172/2090-7214.1000222
Copyright: © 2016 Singh, et al. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.
The OHVIRA syndrome classically occurs in the setting of uterine didelphys or more rarely, a septate uterus with incidence in various case series is 0.1-3.8%. Renal agenesis is the most commonly reported urologic anomaly. The typical patient with this rare condition usually presents after menarche with nonspecific symptoms of recurrent pelvic pain or dysmenorrhea but both of our patients had atypical presentation. Sonography is frequently the initial imaging modality for evaluation of suspected Müllerian duct anomalies, MR imaging is an excellent modality for evaluating the frequently complex Müllerian duct anomalies. Treatment invariably requires surgical intervention in the form of excision of vaginal septum to relieve obstruction. In addition to relief of pain due to obstruction, surgery also reduces chances of pelvic endometriosis due to retrograde menstrual seeding. We are reporting these cases being their atypical presentation in adulthood life.