Isolated Unilateral Absence of Pulmonary Artery (UAPA) in the Adult: Between Simple Cough and Intensive Care
Received Date: May 21, 2018 / Accepted Date: May 25, 2018 / Published Date: May 31, 2018
Unilateral absence of pulmonary artery (UAPA) is a rare congenital condition occurring isolated or in conjunction with other congenital heart defects (CHD). While none-isolated UAPA is mostly detected early in life, detection of isolated UAPA is often delayed due to diverse and unspecific symptoms. While there is consensus on the therapeutic strategy in young symptomatic patients, the incidental finding of UAPA in young or adult asymptomatic patients is a matter of on-going debate and limited evidence. Here, we will present two previously unpublished, illustrative cases with different extent of symptom severity and discuss the difficulties in determining an appropriate therapeutic strategy. Along with the cases, we will review the literature, present typical symptoms and possible pitfalls, and provide an overview of therapeutic options with a focus on the adult patient.
Keywords: Isolated unilateral absence of pulmonary artery (UAPA); Pulmonary hypertension; Pneumonectomy; Revascularization; Hemoptysis
Citation: Jacob FJ, Vogt FM, Stahlberg E, Oechtering TH, Anton S, et al. (2018) Isolated Unilateral Absence of Pulmonary Artery (UAPA) in the Adult: Between Simple Cough and Intensive Care. J Pulm Respir Med 8: 457. Doi: 10.4172/2161-105X.1000457
Copyright: © 2018 Jacob FJ, et al. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.
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