Left Ventricular Pseudo-Aneurism after Transapical Aortic Cannulation in Ehlers-Danlos Syndrome Type IV: A Case ReportTakamitsu Terasaki1, Tamaki Takano1*, Kazunori Komatsu2 and Kenji Okada2
- *Corresponding Author:
- Tamaki Takano
Department of Cardiovascular Surgery
Nagano Red Cross Hospital
Nagano 380-8582, Japan
E-mail: [email protected]p
Received Date: October 07, 2015; Accepted Date: October 16, 2015; Published Date: October 21, 2015
Citation: Terasaki T, Takano T, Komatsu K, Okada K (2015) Left Ventricular Pseudo-Aneurism after Transapical Aortic Cannulation in Ehlers- Danlos Syndrome Type IV: A Case Report. J Vasc Med Surg 3:224. doi:10.4172/2329-6925.1000224
Copyright: © 2015 Strong MJ, et al. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.
Introduction: We report a case of Ehlers-Donlos syndrome which raised left ventricular pseudo-aneurism at the site of transapical aortic cannulation after acute aortic dissection repair. Case Report: A 49-year-old male underwent total arch replacement for type A aortic dissection using transapical aortic cannulation. CT revealed a pseudoaneurysm at the left ventricular apex 2 weeks after the initial surgery, and the size of pseudoaneurysm increased in another 2 weeks. We performed reoperation and found suture dehiscence of transapical cannulation closure. Post-operative course was uneventful. He was diagnosed as Ehlers-Donlos syndrome by genetic examination after the second surgery. Conclusion: Ehlers-Danlos syndrome might be attributed to vulnerability of cardiac muscle and suture dehiscence, and transapical cannulation should be carefully applied in the patients with Ehlers-Danlos syndrome.