Peripheral Nerve Sheath Tumour of Neck: A Rare Presentation a Case Report
- *Corresponding Author:
- Sandeep Kumar Kar
Department of Cardiac Anaesthesiology
Institute of Postgraduate Medical
Education and Research, Kolkata, India
Tel: 033 2204 1100
E-mail: [email protected]
Received Date: December 22, 2015; Accepted Date: April 18, 2016; Published Date: April 20, 2016
Citation: Ganguly T, Kar SK, Bhattacharyya R, Mitra M, Kamat SS, et al. (2016) Peripheral Nerve Sheath Tumour of Neck: A Rare Presentation. J Mol Biomark Diagn S2:016. doi:10.4172/2155-9929.S2-016
Copyright: © 2016 Kar SK, et al. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.
Malignant peripheral nerve sheath tumour (MPNST) is a rare and very aggressive tumour of nerve cell origin associated with poor prognosis. Incidence of MPNST is 1 per 1, 00,000 populations and it constitutes between 3%-10% of all soft tissue sarcomas1-4. MPNST have been found to be associated with neurofibromatosis type 1 (associated with mutation in NF-1 gene) in 2%-29% cases . Male and female are almost equally (53:47) involve. These tumours often create diagnostic dilemmas because of non-specific clinical diagnostic criteria, histopathological resemblance with other spindle cell sarcomas like monophasic synovial sarcoma, leiomyosarcoma and fibrosarcoma.