Primary Spinal Epidural Rhabdomyosarcoma of the Upper Thoracic Spine
|Bouali Sofiene*, Bouhoula Asma, Boubaker Adenane, Maatar Nidhal, Ben Said Kallel Jalel, Aouij Lassaad and Jemel Hafedh|
|Department of Neurosurgery, National Institute of Neurology Tunis, Tunisia|
|Corresponding Author :||Bouali Sofiene
Department of Neurosurgery
National Institute of Neurology Tunis
Tunisia Faculty of Medicine
University of Tunis el MANAR, Tunisia
E-mail: [email protected]
|Received September 15, 2014; Accepted November 17, 2014; Published November 19, 2014|
|Citation: Sofiene B, Asma B, Adenane B, Nidhal M, Jalel BSK,et al. (2014) Primary Spinal Epidural Rhabdomyosarcoma of the Upper Thoracic Spine. J Spine 3:193. doi:10.4172/2165-7939.1000193|
|Copyright: © 2014 Sofiene B, et al. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.|
Introduction: Rhabdomyosarcoma is a highly aggressive and rapidly growing sarcoma with skeletal origin that occasionally appears in the spinal epidural space.
Method: We report a 20-year-old girl who presented with back pain, progressive paraparesis, and urinary retention. She had muscular weakness in her lower extremities and absent deep tendon reflex. An epidural dumbbell-shape mass at T3-T4 level was observed on MRI. The patient underwent T3-T5 hemilaminectomy.
Result: Histopathological examination Immunohistochemical staining confirmed the diagnosis of alveolar Rhabdomyosarcoma. She received radiotherapy and chemotherapy. The patient died 3 months after.
Conclusion: Primary spinal epidural RMS is an extremely rare and very aggressive tumor. The treatment should focus on extensive resection with intensive combination of radiotherapy and chemotherapy.