Pulmonary Atresia with Intact Ventricular Septum: Management Options and Decision-making
Henry Burkholder* and Duraisamy Balaguru
Division of Pediatric Cardiology, University of Texas Houston Medical School, Houston, TX 77030, USA
- *Corresponding Author:
- Henry Burkholder
Division of Pediatric Cardiology
University of Texas Houston Medical School
6410 Fannin Street, UTPB–425, Houston
TX 77030, USA
Tel: 713-500 5738
Fax: 713-500 5751
E-mail: [email protected]
Received Date: February 21, 2012; Accepted Date: December 17, 2012; Published Date: December 19, 2012
Citation: Burkholder H, Balaguru D (2012) Pulmonary Atresia with Intact Ventricular Septum: Management Options and Decision-making. Pediat Therapeut S5:007. doi: 10.4172/2161-0665.S5007
Copyright: © 2012 Burkholder H, et al. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.
Pulmonary atresia with intact ventricular septum (PA-IVS) is a complex congenital heart malformation with a diverse set of anatomical and clinical findings. The incidence is 4.1 per 100,000 live births and is less than 1% of all congenital heart disease. During embryogenesis, PA-IVS is postulated to occur after development of ventricular septum which is later than the development of PA with ventricular septal defect. Every case of PA-IVS poses a considerable challenge to the pediatric cardiologist and cardiovascular surgeon. Although echocardiography is often the first line tool in cardiac imaging, cardiac catheterization is the gold standard for diagnosing PA-IVS and describing the important anatomical features that determine the plan of treatment. This article will focus on the management options and decision making from the interventional cardiologists point of view.