Swelling of Extremities: Primary Lymphedema?
- *Corresponding Author:
- González L
Hospital Rio Hortega Valladolid, Spain
E-mail: [email protected]
Received Date: June 29, 2012; Accepted Date: September 24, 2012; Published Date: September 26, 2012
Citation: González L, Alcalde C, Puente S, Velasco R, García P, et al. (2012) Swelling of Extremities: Primary Lymphedema? Pediat Therapeut 2:135. doi:10.4172/2161-0665.1000135
Copyright: © 2012 González L, et al. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.
Background: Primary lymphedema is a rare disorder, affecting mainly pediatric patients. It results from maldevelopment of the lymphatic vasculature. Its differential diagnosis is wide and includes secondary lymphedema (the most frequent), and several syndromes.
Methods: We report the case of an 8 month old girl who presents primary lymphedema, and we review the literature published on the topic.
Conclusions: Diagnosis of primary lymphedema might be difficult since several syndromes might present swelling. We have recently diagnosed a case of primary lymphedema. Since it is a pretty rare disorder we find it interesting for the scientific community, to learn about it. Besides, we want to emphasize the fact that performing nuclear medicine before magnetic resonance or computed tomography, avoids sedation and risk associated, hence it should be the first test to be performed. The second fact to stress is that an accurate diagnosis might be made by an adult-specialized nuclear medicine service, avoiding the inconvenience of going to a pediatric centre which might be far in distance.