alexa Auditory neuropathy: clinical characteristics and therapeutic approach.
Medicine

Medicine

Journal of Communication Disorders, Deaf Studies & Hearing Aids

Author(s): Raveh E, Buller N, Badrana O, Attias J, Raveh E, Buller N, Badrana O, Attias J, Raveh E, Buller N, Badrana O, Attias J, Raveh E, Buller N, Badrana O, Attias J

Abstract Share this page

Abstract PURPOSE: Auditory neuropathy is characterized by congenital sensorineural hearing loss associated with absent or impaired auditory brainstem evoked responses and preservation of outer hair cell activity. This study describes the recent experience of our tertiary pediatric center with auditory neuropathy (AN). METHODS: The files of all children diagnosed with AN at our center from 2000 to 2005 were reviewed for background data, associated factors, laboratory and audiometry findings, management, and outcome. RESULTS: Mean age at diagnosis was 13 months. Factors known to be associated with AN were found in 18 children, namely, prematurity, hyperbilirubinemia, parental consanguinity, or positive family history. Conception by in vitro fertilization was an additional factor not previously reported. The hearing loss was mostly moderate to severe, and bilateral in all patients but one. Otoacoustic emissions and/or cochlear microphonics were demonstrated in all cases. Hearing improved spontaneously in 4 patients. Management with a hearing aid was successful in 1 of 19 patients. Twelve patients received cochlear implants with good outcome. CONCLUSION: Because neonates with AN have normal otoacoustic emissions and/or cochlear microphonics, screening tests for high-risk neonates should be complemented by auditory brainstem evoked responses to avoid false-negative findings. Because AN is considered a retrocochlear lesion, with normal outer hair cell function, rehabilitation with hearing aids is problematic. Although the level of pathology is apparently at the cochlear nerve, cochlear implantation is often a good solution for failures of conventional rehabilitation. However, our finding of spontaneous improvement in a small subgroup raises questions regarding implantation before age 1 year. This article was published in Am J Otolaryngol and referenced in Journal of Communication Disorders, Deaf Studies & Hearing Aids

Relevant Expert PPTs

Peer Reviewed Journals
 
Make the best use of Scientific Research and information from our 700 + peer reviewed, Open Access Journals
International Conferences 2017-18
 
Meet Inspiring Speakers and Experts at our 3000+ Global Annual Meetings

Contact Us

Agri & Aquaculture Journals

Dr. Krish

[email protected]

1-702-714-7001Extn: 9040

Biochemistry Journals

Datta A

[email protected]

1-702-714-7001Extn: 9037

Business & Management Journals

Ronald

[email protected]

1-702-714-7001Extn: 9042

Chemistry Journals

Gabriel Shaw

[email protected]

1-702-714-7001Extn: 9040

Clinical Journals

Datta A

[email protected]

1-702-714-7001Extn: 9037

Engineering Journals

James Franklin

[email protected]

1-702-714-7001Extn: 9042

Food & Nutrition Journals

Katie Wilson

[email protected]

1-702-714-7001Extn: 9042

General Science

Andrea Jason

[email protected]

1-702-714-7001Extn: 9043

Genetics & Molecular Biology Journals

Anna Melissa

[email protected]

1-702-714-7001Extn: 9006

Immunology & Microbiology Journals

David Gorantl

[email protected]

1-702-714-7001Extn: 9014

Materials Science Journals

Rachle Green

[email protected]

1-702-714-7001Extn: 9039

Nursing & Health Care Journals

Stephanie Skinner

[email protected]

1-702-714-7001Extn: 9039

Medical Journals

Nimmi Anna

[email protected]

1-702-714-7001Extn: 9038

Neuroscience & Psychology Journals

Nathan T

[email protected]

1-702-714-7001Extn: 9041

Pharmaceutical Sciences Journals

Ann Jose

[email protected]

1-702-714-7001Extn: 9007

Social & Political Science Journals

Steve Harry

[email protected]

1-702-714-7001Extn: 9042

 
© 2008- 2017 OMICS International - Open Access Publisher. Best viewed in Mozilla Firefox | Google Chrome | Above IE 7.0 version
adwords