| case |
sex |
BW(kg) |
onset age(d) |
accompanied
abnormalities |
Insulin
initial dosage（u/kg/d） |
Glibenclamide
mg/kg/d |
| 1 |
male |
2.5 |
116 |
multiple epiphyseal dysplasia an episode of acute liver failure isolated central hypothyroidism |
1.2 |
|
| 2 |
male |
2.25 |
50 |
muscle weakness, motor and intelligent developmental delay |
1.3 |
0.9 |
| 3 |
male |
2.01 |
38 |
muscle weakness, motor and intelligent developmental delay |
1.5 |
0.9 |
| 4 |
female |
2.15 |
66 |
|
1.2 |
|
| 5 |
female |
2.4 |
135 |
|
|
|
| 6 |
female |
2.9 |
150 |
|
1.2 |
1.0,partial effective |
| 7 |
female |
3.2 |
90 |
|
1.4 |
unresponsive |
| 8 |
male |
3 |
170 |
|
|
|
| 9 |
male |
2.6 |
90 |
|
1.2 |
|
| 10 |
female |
3.5 |
165 |
|
1.1 |
unresponsive |
|
