1. FXRD1_HUMAN FAD-dependent oxidoreductase domain-containing protein 1
2. MIMIT_HUMAN Mimitin;  Myc-induced mitochondrial protein
NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2
3. NDUA1_HUMAN NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 1
4. NDUAB_HUMAN NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 11
5. NDUF3_HUMAN NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3
6. NDUF4_HUMAN NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4
Hormone-regulated proliferation-associated protein of 20 kDa
7. NDUF5_HUMAN NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5
8. NDUF6_HUMAN NADH dehydrogenase (ubiquinone) complex I, assembly factor 6;  Putative phytoene synthase
9. NDUS1_HUMAN NADH-ubiquinone oxidoreductase 75 kDa subunit, mitochondrial
10. NDUS2_HUMAN NADH dehydrogenase [ubiquinone] iron-sulfur protein, mitochondrial
11. NDUS4_HUMAN NADH dehydrogenase [ubiquinone] iron-sulfur protein, mitochondrial
12. NDUS7_HUMAN NADH dehydrogenase [ubiquinone] iron-sulfur protein, mitochondrial
13. NDUV1_HUMAN NADH dehydrogenase [ubiquinone] flavoprotein 1, mitochondrial
14. NU3M_HUMAN NADH-ubiquinone oxidoreductase chain 3
15. NU5M_HUMAN NADH-ubiquinone oxidoreductase chain 5
16. NU6M_HUMAN NADH-ubiquinone oxidoreductase chain 6
17. NUBPL_HUMAN Iron-sulfur protein NUBPL;  IND1 homolog;  Nucleotide-binding protein-like
Table 5: MT–C1D 17 proteins that have some indication that some polymorphisms may lead to an increased susceptibility to develop Mitochondrial complex 1 deficiency (MT-C1D). Swiss-Prot protein ID and descriptive names shown.
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