1. |
ADT1_HUMAN |
ADP/ATP translocase 1; ADP,ATP carrier protein, heart/skeletal muscle isoform T1 |
2. |
COASY_HUMAN |
Dephospho-CoA kinase |
Bifunctional coenzyme A synthase |
3. |
COQ2_HUMAN |
4-hydroxybenzoate polyprenyltransferase, mitochondrial |
4. |
CS012_HUMAN |
Protein C19orf12 |
5. |
DDIT4_HUMAN |
DNA damage-inducible transcript 4 protein; HIF-1 responsive protein RTP801; |
Protein regulated in development and DNA damage response 1 |
6. |
DPOG2_HUMAN |
DNA polymerase subunit gamma-2, mitochondrial; |
Mitochondrial DNA polymerase accessory subunit |
7. |
FXRD1_HUMAN |
FAD-dependent oxidoreductase domain-containing protein 1 |
8. |
KLK6_HUMAN |
Kallikrein-6; Neurosin; Protease M; Serine protease 18; Serine protease 9 |
9. |
MIMIT_HUMAN |
Mimitin; Myc-induced mitochondrial protein; |
NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 |
10. |
NDUA1_HUMAN |
NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 1 |
11. |
NDUAB_HUMAN |
NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 11 |
12. |
NDUF3_HUMAN |
NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 |
13. |
NDUF4_HUMAN |
NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 |
Hormone-regulated proliferation-associated protein of 20 kDa |
14. |
NDUF5_HUMAN |
NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 |
15. |
NDUF6_HUMAN |
NADH dehydrogenase (ubiquinone) complex I, assembly factor 6; Putative phytoene synthase |
16. |
NDUS1_HUMAN |
NADH-ubiquinone oxidoreductase 75 kDa subunit, mitochondrial |
17. |
NDUS2_HUMAN |
NADH dehydrogenase [ubiquinone] iron-sulfur protein, mitochondrial |
18. |
NDUS4_HUMAN |
NADH dehydrogenase [ubiquinone] iron-sulfur protein, mitochondrial |
19. |
NDUS7_HUMAN |
NADH dehydrogenase [ubiquinone] iron-sulfur protein, mitochondrial |
20. |
NDUV1_HUMAN |
NADH dehydrogenase [ubiquinone] flavoprotein 1, mitochondrial |
21. |
NU3M_HUMAN |
NADH-ubiquinone oxidoreductase chain 3 |
22. |
NU5M_HUMAN |
NADH-ubiquinone oxidoreductase chain 5 |
23. |
NU6M_HUMAN |
NADH-ubiquinone oxidoreductase chain 6 |
24. |
NUBPL_HUMAN |
Iron-sulfur protein NUBPL; IND1 homolog; Nucleotide-binding protein-like |
25. |
PEO1_HUMAN |
Twinkle protein; Progressive external ophthalmoplegia 1 protein; |
T7 gp4-like protein with intra-mitochondrial nucleoid localization; |
T7-like mitochondrial DNA helicase |
26. |
RIR2B_HUMAN |
Ribonucleoside-diphosphate reductase subunit M2 B |
TP53-inducible ribonucleotide reductase M2 B |
p53-inducible ribonucleotide reductase small subunit 2-like protein |