1. ADT1_HUMAN ADP/ATP translocase 1;  ADP,ATP carrier protein, heart/skeletal muscle isoform T1
2. COASY_HUMAN Dephospho-CoA kinase
Bifunctional coenzyme A synthase
3. COQ2_HUMAN 4-hydroxybenzoate polyprenyltransferase, mitochondrial
4. CS012_HUMAN Protein C19orf12
5. DDIT4_HUMAN DNA damage-inducible transcript 4 protein; HIF-1 responsive protein RTP801;
Protein regulated in development and DNA damage response 1
6. DPOG2_HUMAN DNA polymerase subunit gamma-2, mitochondrial; 
Mitochondrial DNA polymerase accessory subunit
7. FXRD1_HUMAN FAD-dependent oxidoreductase domain-containing protein 1
8. KLK6_HUMAN Kallikrein-6;  Neurosin; Protease M; Serine protease 18; Serine protease 9
9. MIMIT_HUMAN Mimitin;  Myc-induced mitochondrial protein;
NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2
10. NDUA1_HUMAN NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 1
11.   NDUAB_HUMAN NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 11
12.   NDUF3_HUMAN NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3
13.   NDUF4_HUMAN NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4
Hormone-regulated proliferation-associated protein of 20 kDa
14.   NDUF5_HUMAN NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5
15.   NDUF6_HUMAN NADH dehydrogenase (ubiquinone) complex I, assembly factor 6;  Putative phytoene synthase
16.    NDUS1_HUMAN NADH-ubiquinone oxidoreductase 75 kDa subunit, mitochondrial
17.   NDUS2_HUMAN NADH dehydrogenase [ubiquinone] iron-sulfur protein, mitochondrial
18.   NDUS4_HUMAN NADH dehydrogenase [ubiquinone] iron-sulfur protein, mitochondrial
19.   NDUS7_HUMAN NADH dehydrogenase [ubiquinone] iron-sulfur protein, mitochondrial
20.    NDUV1_HUMAN NADH dehydrogenase [ubiquinone] flavoprotein 1, mitochondrial
21.   NU3M_HUMAN NADH-ubiquinone oxidoreductase chain 3
22.   NU5M_HUMAN NADH-ubiquinone oxidoreductase chain 5
23.   NU6M_HUMAN NADH-ubiquinone oxidoreductase chain 6
24.   NUBPL_HUMAN Iron-sulfur protein NUBPL;  IND1 homolog;  Nucleotide-binding protein-like
25.   PEO1_HUMAN Twinkle protein; Progressive external ophthalmoplegia 1 protein;
T7 gp4-like protein with intra-mitochondrial nucleoid localization;
T7-like mitochondrial DNA helicase
26.   RIR2B_HUMAN Ribonucleoside-diphosphate reductase subunit M2 B
TP53-inducible ribonucleotide reductase M2 B
p53-inducible ribonucleotide reductase small subunit 2-like protein
Table 6: MITOCHOND NOT PARK 26 proteins that have some connection with the mitochondria but are not in the PARK set. Swiss-Prot protein ID and descriptive names shown.
Goto home»