Gender (males: females) 7:12
Age (years old) 47 [17-83]
Presenting features  
Age at onset (years)* 35 [0.67-62]
Age at diagnosis (years) 44 [15-70]
Time between the onset and diagnosis (years) 16 [3-48]
Follow-up from diagnosis (years)§ 3 [0.6-18]
Disease manifestations  
Pruritus 14 (74%)
Cutaneous 19 (100%)
Gastrointestinal 16 (84%)
Osteoarticular 14 (74%)
Neuropsychiatric 9 (47%)
Allergic 10 (53%)
Cardiovascular 9 (47%)
Skin lesions  
Generalized 2 (11%)
Restricted to one area 6 (32%)
More than one area involved, but not generalized 11 (58%)
Laboratory findings at presentation  
Total IgE (KU/L) 10.3 [<2-231]
Tryptase (mg/L)§ 24.9 [4-305]
Results are expressed as median [range] values, absolute numbers and (percentages).
*Date of the first mast cell mediators release episode or appearance of skin lesions
Date of the first bone marrow study or skin biopsy
Normal values: IgE<100 KU/L
§Normal values: Tryptase<13.5 μg/L
Table 2: Clinical and laboratory characteristics from the patients included in this study.
Goto home»