Cleidocranial dysplasia is also known as Scheuthauer-Marie-Sainton Syndrome. It is a rare disease which can occur in either sex equally or by autosomal dominant trait. Problems associated with this condition are multiple supernumerary teeth, retained deciduous teeth, delayed eruption, change in shape, impacted teeth and absence of deciduous teeth resorption. By profession pediatric dentist is the person who identifies the retained deciduous teeth and delay in eruption or absence of permanent teeth. Here we report a rare case of cleidocranial dysplasia in a 25 year old female patient and interdisciplinary management.