Splenic involvement in hydatid disease is uncommon, representing less than 2% of all human infestations by Echinococcus. It is an endemic disease in the sheep and cattle raising countriesMiddle East, North Africa, New Zealand, Australia, and South America. In India, the recorded prevalence of the splenic hydatid cyst is 2.5%, with the highest incidence reported in the central parts. In areas of endemic hydatid disease, most of these cysts are due to the larval form of this parasite, whereas non-parasitic cysts comprise the vast majority in Western countries.The first case of a splenic hydatid cyst was reported by Berlot in 1790 from an autopsy. Herein, we report a case of splenic hydatid disease in a 18 year old male form Haryana (India). We report this case because of its rarity.