Ossifying fibroma is a rare fibro-osseous lesion that most commonly occurs in the craniofacial skeleton, with particular predilection for the nasal cavity, paranasal sinuses, and the orbit (Chung EM Radiographics 2008). Psammomatoid ossifying fibroma (POF), also known as juvenile (active) ossifying fibroma, is a variant of ossifying fibroma containing numerous calcified "psammomatoid" ossicles that histologically resemble psammoma bodies. A more common and related variant is the cementifying or cementoossifying fibroma, which occurs in gnathic bones (Slootweg PJ J Oral Pathol Med 1994, Kuta JA AJNR 1995, Kasliwal MK J Neurosurg Pediatrics 2011). Very few cases of POF have been described in the literature; most of them involve the paranasal sinuses or the orbit (Margo CE Ophtalmology 1985, Han MH AJNR 1991, Wenig BM Cancer 1995). We describe an unusual case of POF involving the maxillary sinus in a child who presented with swelling in the left facial region. The appearance of the lesion and its location presented a diagnostic challenge. To the best of our knowledge, a POF involving the maxillary sinus with intracranial extension was not previously reported.
Last date updated on July, 2014