Head and neck sarcomas are rare tumors, accounting for only 1% of all head and neck malignancies and 5% of all sarcomas. They are a heterogeneous group of neoplasms according to their origin site that can be bone, muscle, vessel, nerve, fat and fibrous tissue. Most common histological types are: osteosarcoma, rhabdomyosarcoma, pleomorphic sarcoma and angiosarcoma. The treatment depended on histological type, grade, stage and operative considerations according to the site. They are characterized by high rate of local recurrence and lower overall survival rate because of anatomic constraints limiting functional resections rather than difference in biologic behavior and tumor histology. Given to their management difficulties, they must be treated in multi-disciplinary approach.
Last date updated on January, 2021