Abstract

Peritoneal pseudomyxoma (PMP) is a very rare and complex condition characterized by gelatinous ascites with mucinous epithelial implants on the peritoneal surfaces. It classically results from the rupture of an appendicular mucinous tumor in 90% of cases, more rarely from an ovarian tumor. This disease mainly affects women. Its incidence is estimated at 2 cases per million inhabitants. Because of its indolent character, PMP is often discovered at an advanced stage during laparotomy or imaging studies for other medical problems. The CT scan is the best examination to establish the diagnosis by highlighting the pathognomonic signs of gelatinous ascites. Its diagnosis is confirmed intra operatively by anatomopathological study. Cytoreduction surgery associated with intraperitoneal chemotherapy is the gold standard for the management of this disease.