Concurrent Splenic Lymphangiomatosis And Proteus Syndrome | 16407
Journal of Clinical & Experimental Pathology
Like us on:
Our Group organises 3000+ Global Conferenceseries Events every year across USA, Europe & Asia with support from 1000 more scientific Societies and Publishes 700+ Open Access Journals which contains over 50000 eminent personalities, reputed scientists as editorial board members.
A37-year-old female presented with Proteus syndrome and was found to have an asymptomatic enlarged spleen. Pathology
confirmed splenic lymphangiomatosis. Proteus syndrome is a rare congenital disorder. It was named after the Greek god
Proteus, meaning ?The Polymorphous?, for he could avoid capture by altering his shape. It can manifest usually as progressive
skeletal abnormalities including asymmetric overgrowth, macrodactyly, scoliosis, and limb length discrepancy followed by
soft tissue anomalies namely fatty, muscular, lymphatic and vascular malformations. Visceral malformations are rare including
splenomegaly. In this case report, we highlight the rare association of this syndrome with lymphangiomatosis in the Middle-
Reja Syed Emran completed her Bachelors of Medicine and Surgery (MBBS) Degree from Army medical College, Pakistan at the age of 23 and is currently residing
in Saudi Arabia, and an intern at King Faisal Specialist Hospital & Research Center, Riyadh. She has participated and assisted in research projects, and published
a case report with her colleagues while rotating in the Department of General Surgery.
Peer Reviewed Journals
Make the best use of Scientific Research and information from our 700 + peer reviewed, Open Access Journals